Cochlear Implantation for Children with Single-Sided Deafness
Anna, a 3-year-old girl, was a product of a full-term pregnancy without complications. She passed newborn hearing screening in the right ear and was referred in the left ear prior to discharge from the nursery. She was subsequently seen for a diagnostic auditory brainstem response (ABR) evaluation, which was consistent with hearing within normal limits in the right ear and a severe to profound sensorineural hearing loss in the left ear. Etiology of this hearing loss was unknown. She did undergo genetic testing, which did not identify any known mutations.
Shortly after her diagnosis, Anna was fitted with a hearing aid in the left ear that she wore until recently and subsequently rejected. English is not her primary language, but she is exposed to it at home. Anna is otherwise in good general health. There were no cognitive issues suspected from her evaluations.