Cochlear Implantation in a Child with Single-Sided Deafness
HN was born full term with the complication of maternal hemorrhage. He required a 4-day neonatal intensive care unit (NICU) stay and was diagnosed with bicuspid aortic valve and dilated ascending aorta. He passed his newborn hearing screen in the right ear and referred twice in the left. There was no reported family history of hearing loss. There were no concerns about speech and language development as HN was scoring above average on standardized speech evaluations. From age 2 to 3 years, HN had significant issues with chronic otitis media and was referred to an ear, nose, and throat (ENT) physician for pressure equalizing (PE) tubes. PE tubes were inserted when the patient was 4 years old.
At 2 months of age, auditory brainstem response (ABR) testing was performed using unmasked click stimuli in each ear. Thresholds were determined to be within normal limits (15 dB) bilaterally, and no further testing was recommended. Immediately following HN’s PE tube surgery at the age of 4 years, a diagnostic ABR was performed. The ABR revealed normal auditory sensitivity in the right ear, and no responses to the output limits of the equipment in the left ear to click, tone burst, and masked bone conduction stimuli. Distortion product otoacoustic emissions (DPOAEs) were present in the right ear and absent in the left.